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Cardiology2 papers

Quadricuspid aortic valve

Last edited: 4/23/2026

Overview

Quadricuspid aortic valve is a rare congenital anomaly characterized by the presence of four leaflets instead of the usual three in the aortic valve, potentially leading to valvular dysfunction and hemodynamic disturbances 1.

Diagnosis

  • Echocardiography is essential for diagnosis, revealing the characteristic four-leaflet configuration 1.
  • Cardiac MRI or CT angiography may be used to assess valve morphology and associated anomalies 1.
  • Hemodynamic assessment via echocardiography to evaluate for regurgitation or stenosis 1.
  • Management

  • Surgical repair: Recommended for complex lesions to preserve native valve function 1.
  • Aortic valve replacement (AVR): Indicated for patients with severe valvular dysfunction or complex lesions not amenable to repair 1.
  • Follow-up: Regular echocardiographic monitoring post-surgery to assess outcomes and complications 1.
  • Special Populations

  • Pregnancy: Limited data; management typically focuses on addressing underlying valvular dysfunction with surgical intervention if necessary 1.
  • Pediatrics: Specific management strategies are not detailed in the provided abstracts; surgical intervention may be required based on severity 1.
  • Elderly: Considerations for surgical risk and prosthetic valve choice are crucial; AVR may be preferred in cases of severe dysfunction 1.
  • Comorbidities: Presence of comorbidities may influence surgical approach and prosthetic valve selection; tailored management is advised 1.
  • Key Recommendations

  • Consider surgical repair for simple lesions to preserve native valve when feasible 1 (Evidence: Moderate).
  • Perform aortic valve replacement for complex lesions or severe valvular dysfunction 1 (Evidence: Moderate).
  • Regular postoperative echocardiographic follow-up is essential to monitor valve function and detect complications early 1 (Evidence: Moderate).
  • References

    1 Prêtre R, Faidutti B. Surgical management of aortic valve injury after nonpenetrating trauma. The Annals of thoracic surgery 1993. link90708-p)

    Original source

    1. [1]
      Surgical management of aortic valve injury after nonpenetrating trauma.Prêtre R, Faidutti B The Annals of thoracic surgery (1993)

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