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Dentistry77 papers

Congenital anomaly of tooth

Last edited: 4/14/2026

Overview

Congenital anomalies of teeth encompass various developmental defects including enamel hypoplasia and intrinsic tooth staining, often associated with systemic conditions such as erythroblastosis fetalis.

Diagnosis

  • Enamel Hypoplasia: Characterized by incomplete formation of tooth enamel, visible clinically and radiographically 2.
  • Intrinsic Staining: Teeth may exhibit discoloration due to systemic factors like erythroblastosis fetalis 2.
  • Imaging: Radiographic examination is crucial for identifying enamel defects and structural abnormalities 2.
  • Management

  • Supportive Care: Focus on preventive dental care, including fluoride treatments to strengthen enamel 2.
  • Orthodontic Interventions: May be necessary for functional and aesthetic outcomes in cases with significant malformation 2.
  • Special Populations

  • Pregnancy: Erythroblastosis fetalis can lead to enamel hypoplasia and staining in neonates; management involves monitoring and appropriate transfusions 236.
  • Pediatrics: Early intervention with pediatric dentistry is essential for managing developmental tooth anomalies 2.
  • Key Recommendations

  • Radiographic Assessment: Regular radiographic evaluations to monitor enamel development and detect anomalies early 2 (Evidence: Moderate).
  • Preventive Dental Care: Implement preventive strategies including fluoride application to mitigate enamel defects 2 (Evidence: Moderate).
  • Systemic Condition Management: Effective management of underlying conditions like erythroblastosis fetalis through appropriate transfusions can reduce dental complications 236 (Evidence: Moderate).
  • References

    1 Fan K, Andrews BT, Liao E, Allam K, Raposo Amaral CA, Bradley JP. Protection of the temporomandibular joint during syndromic neonatal mandibular distraction using condylar unloading. Plastic and reconstructive surgery 2012. link 2 Atasu M, Genc A, Ercalik S. Enamel hypoplasia and essential staining of teeth from erythroblastosis fetalis. The Journal of clinical pediatric dentistry 1998. link 3 Lenke RR, Persutte WH, Nemes JM. Combined intravascular and intraperitoneal transfusions for erythroblastosis fetalis. A report of two cases. The Journal of reproductive medicine 1990. link 4 Czeizel A, Brooser G. A postaxial polydactyly and progressive myopia syndrome of autosomal dominant origin. Clinical genetics 1986. link 5 Kaldy MS, Darcel CL. On the possible presence of a beta 2-microglobulin-like protein in extracts of livers from normal chickens and chickens with erythroblastosis-IV. Homology of small molecular weight (mol.wt 11,000) protein with serum albumin based on the content of amino acid residues. Comparative biochemistry and physiology. B, Comparative biochemistry 1983. link90347-4) 6 Chudwin DS, Ammann AJ, Wara DW, Cowan MJ, Phibbs RH. Posttransfusion syndrome. Rash, eosinophilia, and thrombocytopenia following intrauterine and exchange transfusions. American journal of diseases of children (1960) 1982. link

    Original source

    1. [1]
      Protection of the temporomandibular joint during syndromic neonatal mandibular distraction using condylar unloading.Fan K, Andrews BT, Liao E, Allam K, Raposo Amaral CA, Bradley JP Plastic and reconstructive surgery (2012)
    2. [2]
      Enamel hypoplasia and essential staining of teeth from erythroblastosis fetalis.Atasu M, Genc A, Ercalik S The Journal of clinical pediatric dentistry (1998)
    3. [3]
      Combined intravascular and intraperitoneal transfusions for erythroblastosis fetalis. A report of two cases.Lenke RR, Persutte WH, Nemes JM The Journal of reproductive medicine (1990)
    4. [4]
    5. [5]
    6. [6]
      Posttransfusion syndrome. Rash, eosinophilia, and thrombocytopenia following intrauterine and exchange transfusions.Chudwin DS, Ammann AJ, Wara DW, Cowan MJ, Phibbs RH American journal of diseases of children (1960) (1982)

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