Overview
Autoimmune vasculitis encompasses a spectrum of disorders characterized by inflammation of blood vessels, leading to diverse clinical manifestations depending on the size and location of the affected vessels. These conditions can involve single or multiple organ systems, including skin, kidneys, lungs, and nervous system 1237152028303340475057.Diagnosis
Management
Special Populations
Key Recommendations
References
Showing 100 most recent of 1005 indexed papers.
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Pediatric research 2026. link 6 Zhang Y, Wang Y, Zhao Z, Du H, Zong Y, Cao Y. Integrative Chinese-western therapy for Leukocytoclastic vasculitis-induced refractory leg ulcer: An 8-month healing journey with reduced corticosteroid dependency. Explore (New York, N.Y.) 2026. link 7 Cao D, Liu X. Analysis of Clinical Features and High-Risk Factors of Gastrointestinal Involvement in Children With IgA Vasculitis. Clinical pediatrics 2026. link 8 Rivero-Otamendi E, Navarro-Sánchez V, Hernández-Andrade A, Zavala-Miranda MF, Hinojosa-Azaola A, Sánchez-Mejía DE et al.. Mortality Prediction in Antineutrophil Cytoplasmic Antibody-Associated Vasculitis With Kidney Involvement: Validation of the DANGER Score. Journal of clinical rheumatology : practical reports on rheumatic & musculoskeletal diseases 2026. link 9 Sandino-Bermúdez MJ, Mulia-Soto AS, Mejía-Vilet JM, Martín-Nares E, Hernández-López A, Hinojosa-Azaola A. Factors Associated With Relapses and Performance of the French Vasculitis Study Group Relapse Score in a Cohort of Mexican Patients With Antineutrophil Cytoplasmic Antibody-Associated Vasculitis. Journal of clinical rheumatology : practical reports on rheumatic & musculoskeletal diseases 2026. link 10 Takano K, Hida K, Tani T, Yoshimitsu K. Vasculitis syndromes: large vessel vasculitides and ANCA-associated vasculitides from a neuroradiologist's perspective. Japanese journal of radiology 2026. link 11 Turna ZH. Vasculitis associated with nonhematological malignancies. Current opinion in rheumatology 2026. link 12 Scaglione V, Cola M, Sasset L, Fortarezza F, Casarin C, Trevenzoli M et al.. Leukocytoclastic Vasculitis Induced by Dalbavancin: A Case Report. The American journal of case reports 2026. link 13 Xie J, Shi L, Wang L, Dai J. Commentary: Anti-endothelial cell antibodies in pathogenesis of vasculitis. Frontiers in immunology 2026. link 14 Tou LC, Doyle C, Payne G, Buntyn R, Lamb J. Microscopic Polyangiitis in a Nonagenarian: Diagnostic and Therapeutic Challenges in Geriatric Vasculitis. Annals of geriatric medicine and research 2026. link 15 Mandel DA, Shekhar N, Hanna R, Reddy U. Update on antineutrophil cytoplasmic antibody vasculitis. Current opinion in nephrology and hypertension 2026. link 16 Pallotti F, Mettler C, Papo M, Iudici M, Padoan R, Sorin B et al.. Overlapping forms of granulomatosis with polyangiitis and eosinophilic granulomatosis with polyangiitis: Insights from a European multicenter study. Journal of internal medicine 2026. link 17 Gulati SK, Hung W, Voaklander D, Jones CA, Yacyshyn EA. Comparing incidence of vasculitis between farming, rural and urban population: A population-based study. Clinical rheumatology 2026. link 18 Alba MA, Jennette JC. New insights into clinical spectrum of antineutrophil cytoplasmic autoantibody associated disease. Current opinion in nephrology and hypertension 2026. link 19 Wei Q, Jiang W, Chen X, Cai H, Feng R, Dong S. Leukocytoclastic Vasculitis and Profound Cytopenias Following Teicoplanin Therapy: A Case Report on Glycopeptide Cross-Reactivity. Clinical therapeutics 2026. link 20 Scoglio M, Orlando C, Milani GP, Bianchetti MG, Bronz G, Rizzi M et al.. Vasculopathy and vasculitis associated with levamisole-adulterated cocaine: a systematic review. Journal of autoimmunity 2026. link 21 Shi X, Li Z, Ma X, Zhang B, Wu X, Fan H et al.. Exploring the Vasculitis-Tumors Link: Epidemiological Patterns, Mechanistic Insights, and Clinical Implications. Advanced science (Weinheim, Baden-Wurttemberg, Germany) 2026. link 22 Yamane T, Inoue A, Ichikawa C. Glucocorticoid-free remission with simultaneous mepolizumab and rituximab in life-threatening PR3-ANCA-positive eosinophilic granulomatosis with polyangiitis: a case report and literature review. Clinical rheumatology 2026. link 23 Engelstein DK, Levartovsky D, Wexler ID, Elkan PN, Padeh S, Bieber A et al.. The Natural History of Deficiency of Adenosine Deaminase 2 Vasculitis in a Large Cohort and Factors Associated With Disease-Related Damage. The Journal of rheumatology 2026. link 24 Bayindir Y, Jelusic M, Ozen S. Highlights from the breakout session: vasculitis in paediatric rheumatology. Rheumatology (Oxford, England) 2025. link 25 Kumar S, Narayanan S, Panda PK, Chowdhury A. Possible Terbinafine and/or Itraconazole Induced Vasculitis - A Case Study. Current drug safety 2025. link 26 Hansen-Abeck I, Rünger A, Piepke L, Kött J, Giordano-Rosenbaum A, Menz A et al.. Characterization of non-IgA vasculitis: Demographic, clinical, and treatment-related features in a retrospective analysis of 28 biopsy-confirmed cases from a German university hospital. The Journal of dermatology 2025. link 27 Saro-Buendía M, Mansilla-Polo M, García-Piñero A, Armengot-Carceller M. Stimulator of interferon genes-associated vasculopathy with onset in infancy (SAVI syndrome). European annals of otorhinolaryngology, head and neck diseases 2025. link 28 Pacut P, Gwathmey KG. Top 10 Clinical Pearls in Vasculitic Neuropathies. Seminars in neurology 2025. link 29 Katsumata Y, Sada KE, Kameda T, Dobashi H, Kaname S, Tsuboi N et al.. Comparison of different ANCA detection methods in a predominantly MPO-ANCA-associated vasculitis cohort. Immunological medicine 2025. link 30 Maeda Y, Ikeguchi R, Masui K, Kurata A, Kitagawa K, Shimizu Y. Anti-neutrophil cytoplasmic antibody-associated central nervous system vasculitis mimicking brain tumor: A case report. Neuropathology : official journal of the Japanese Society of Neuropathology 2025. link 31 Benson D. Imaging of Pulmonary Vasculitis. Radiologic clinics of North America 2025. link 32 Gagne SJ, Sivaraman V, Bosman ES, Klamer B, Morishita KA, Huber A et al.. Comparing Rituximab and Cyclophosphamide in Induction Therapy for Childhood-Onset Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis: An ARChiVe Registry Cohort Study. Arthritis care & research 2025. link 33 McLean-Tooke A, Ong J, Kwan A, Krummenacher M, Bundell C. Diagnostic performance of assays for urgent MPO, PR3 and GBM autoantibodies in suspected vasculitis. Pathology 2025. link 34 Fukami S, Ohmura SI, Masui T, Otsuki Y, Yukishima T, Yonezawa H et al.. MRI-guided muscle biopsy improves diagnostic yield in small- to medium-vessel vasculitis: a retrospective single-center study. Rheumatology international 2025. link 35 Ruffer N, Pinal-Fernandez I, Preusse C, Mammen AL, Holzer MT, Kleefeld F et al.. Vasculitic fasciitis characterizes a distinct subset of vasculitic myopathy with interferon-gamma signature. Acta neuropathologica 2025. link 36 Zedde M, Quatrale R, Andreone V, Pezzella FR, Micieli G, Cortelli P et al.. Post-infectious central nervous system vasculitides in adults: an underdiagnosed and treatable disease part II. Neuroimaging of selected etiologies : Part II. Neuroimaging of selected etiologies. Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology 2025. link 37 Hendrickson MJ, Wallace ZS. Mechanisms and Screening for Atherosclerosis in Adults With Vasculitis. Arteriosclerosis, thrombosis, and vascular biology 2025. link 38 Fernandez-Flores A. Concepts in Cutaneous Vasculitis. The American Journal of dermatopathology 2025. link 39 Watanabe K, Shimada N, Kanzaki M, Fukuoka K, Asano K. Late-onset Neutropenia after Rituximab Treatment for MPO-ANCA-associated Vasculitis. Internal medicine (Tokyo, Japan) 2025. link 40 Imai Y, Ota Y, Matsumoto K, Akiyama M, Suzuki K, Kaneko Y. Performance of the 2022 ACR/EULAR Classification Criteria in Comparison With the European Medicines Agency Algorithm in Antineutrophil Cytoplasmic Antibody-Associated Vasculitis. The Journal of rheumatology 2024. link 41 Renuncio-García M, Calvo-Río V, Benavides-Villanueva F, Al Fazazi S, Rodríguez-Vidriales M, Escagedo-Cagigas C et al.. ANCA detection with solid phase chemiluminescence assay: diagnostic and severity association in vasculitis. Immunologic research 2024. link 42 Padilha IG, Nehme A, de Boysson H, Létourneau-Guillon L. Imaging of Vasculitis Associated with Systemic Disease. Neuroimaging clinics of North America 2024. link 43 Hamam O, Cartmell SC, Romero JM. Imaging of Small Artery Vasculitis. Neuroimaging clinics of North America 2024. link 44 Ahn SS, Heo SJ, Ha JW, Park YB, Lee SW. Clinical association of health-related quality of life and mortality in an antineutrophil cytoplasmic antibody-associated vasculitis cohort. Seminars in arthritis and rheumatism 2024. link 45 Pochepnia S, Lang IM, Milos RI, Röhrich S, Ba-Ssalamah A, Beer L et al.. Hughes-Stovin syndrome-An important differential diagnosis in patients with suspected chronic thromboembolic pulmonary hypertension : A case report. Wiener klinische Wochenschrift 2024. link 46 Fadoul MA, Tjaden B, Daneshpooy S, McMackin K. Spontaneous brachial artery pseudoaneurysm secondary to vasculitis. Vascular 2024. link 47 Yang K, Tang J, Li H, Zhang H, Ding J, Li Z et al.. LncRNAs in Kawasaki disease and Henoch-Schönlein purpura: mechanisms and clinical applications. Molecular and cellular biochemistry 2024. link 48 Isoherranen K, Kluger N, Hannula-Jouppi K, Väkevä L. The Role of Negative Pressure Wound Therapy (NPWT) in the Management of Vasculitic Wounds: Case Series of Eight Patients. The international journal of lower extremity wounds 2024. link 49 Coorey CP, Aarabi A, Kumar K. Mixed cryoglobulinaemia vasculitis secondary to marginal zone lymphoma in a patient with end-stage renal failure on haemodialysis. CEN case reports 2024. link 50 Nunes RH, Corrêa DG, Pacheco FT, Fonseca APA, Hygino da Cruz LC, da Rocha AJ. Neuroimaging of Infectious Vasculopathy. Neuroimaging clinics of North America 2024. link 51 Sherri A, Mortada MM, Makowska J, Lewandowska-Polak A. Primary angiitis of the CNS and ANCA-associated vasculitis: from pathology to treatment. Rheumatology international 2024. link 52 Korkmaz C, Yıldırım R, Dinler M, Cansu DU. Coexistence of IgG4-related disease and ANCA-associated vasculitis: case report and review of the literature. Rheumatology international 2024. link 53 Saha MK. Overview of Vasculitides in Adults. Neuroimaging clinics of North America 2024. link 54 Sawhney S. Childhood Vasculitis. Indian journal of pediatrics 2024. link 55 Nomura S, Shimojima Y, Ichikawa T, Miyazaki D, Uruha A, Kishida D et al.. Immunopathological features of myopathy associated with small-to-medium-sized vessel vasculitis and differences from autoimmune myositis. Clinical and experimental rheumatology 2024. link 56 Yun JD, Lee JH, Pyo JY, Ahn SS, Song JJ, Park YB et al.. Birmingham vasculitis activity score and the short form 36-item health survey predict current depressive disorders in patients with antineutrophil cytoplasmic antibody-associated vasculitis during the SARS-CoV-2 pandemic. Zeitschrift fur Rheumatologie 2024. link 57 Manfredi A, Cassone G, Izzo R, Dallagiacoma G, Felicetti M, Cariddi A et al.. Interstitial lung disease in microscopic polyangiitis and granulomatosis with polyangiitis: demographic, clinical, serological and radiological features of an Italian cohort from the Italian Society for Rheumatology. Clinical and experimental rheumatology 2023. link 58 Ecclestone T, Watts RA. Classification and epidemiology of vasculitis: Emerging concepts. Best practice & research. 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Immunological reviews 2023. link 63 Xiong Q, Lin W, Shen C, Meng T, Tang R, Ooi JD et al.. Coexistence of antineutrophil cytoplasmic antibody (ANCA)-associated vasculitis (AAV) and IgA nephropathy. Immunologic research 2023. link 64 Arnett N, Pavlou A, Burke MP, Cucchiara BL, Rhee RL, Song JW. Vessel wall MR imaging of central nervous system vasculitis: a systematic review. Neuroradiology 2022. link 65 Bazzi N, Salloum A, Chebl JA, Hreibe W, Bazzi M, Fiani E et al.. Juvenile gangrenous vasculitis of the scrotum: systematic review. International journal of dermatology 2022. link 66 Guda VA, Brown ME, Palacios M. Spontaneous ecchymoses. The Journal of family practice 2022. link 67 Carette S. Vasculitis: What Have We Learned in the Last 50 Years?. The Journal of rheumatology 2022. link 68 Pimentel-Quiroz VR, Sánchez-Torres A, Reátegui-Sokolova C, Gamboa-Cárdenas RV, Sánchez-Schwartz C, Medina-Chinchón M et al.. Performance of the 2017 American College of Rheumatology/European League Against Rheumatism Provisional Classification Criteria for Antineutrophil Cytoplasmic Antibody-Associated Vasculitis in a Peruvian Tertiary Care Center. Journal of clinical rheumatology : practical reports on rheumatic & musculoskeletal diseases 2022. link 69 Quan Z, Liu M, Zhao J, Yang X. Correlation between early changes of serum lipids and clinical severity in patients with wasp stings. Journal of clinical lipidology 2022. link 70 Ball-Burack MR, Kosowsky JM. A Case of Leukocytoclastic Vasculitis Following SARS-COV-2 Vaccination. The Journal of emergency medicine 2022. link 71 Takeyama R, Fukuda K, Kouzaki Y, Koga T, Hayashi S, Ohtani H et al.. Intracerebral hemorrhage due to vasculitis following COVID-19 vaccination: a case report. Acta neurochirurgica 2022. link 72 Altun E, Kuzucular E. Leukocytoclastic vasculitis after COVID-19 vaccination. Dermatologic therapy 2022. link 73 Yoon T, Ahn SS, Pyo JY, Song JJ, Park YB, Lee SW. Serum vitamin D level correlates with disease activity and health-related quality of life in antineutrophil cytoplasmic antibody-associated vasculitis. Zeitschrift fur Rheumatologie 2022. link 74 Hecker C, Welponer T, Herold M, Trinka E, Broussalis E, Killer-Oberpfalzer M. Update on treatment strategies for vasculitis affecting the central nervous system. Drug discovery today 2022. link 75 Folci M, Ramponi G, Solitano V, Brunetta E. Serum ANCA as Disease Biomarkers: Clinical Implications Beyond Vasculitis. Clinical reviews in allergy & immunology 2022. link 76 Yanartaş M, Karakoç AZ, Zengin A, Taş S, Olgun-Yildizeli Ş, Mutlu B et al.. Multimodal Approach of Isolated Pulmonary Vasculitis: A Single-Institution Experience. The Annals of thoracic surgery 2022. link 77 Kawashima S, Kishimoto M, Hibino T, Lee H, Sato Y, Komagata Y et al.. MPO-ANCA-positive Microscopic Polyangiitis Following COVID-19 Infection. Internal medicine (Tokyo, Japan) 2022. link 78 Yang S, Chai D, Li Y, Wang Y, Zhan X, Zhang L et al.. Patterns of lung diseases predict survival in patients with MPO-ANCA-associated vasculitis: a single-center retrospective study. Clinical rheumatology 2022. link 79 Meng T, Shen C, Tang R, Lin W, Ooi JD, Eggenhuizen PJ et al.. Clinical features and outcomes of anti-neutrophil cytoplasmic autoantibody-associated vasculitis in Chinese childhood-onset patients. Clinical and experimental medicine 2022. link 80 Yamamoto S, Mukai T, Fujita S, Koide Y, Ono Y, Inubushi M et al.. The "Ant-farm"-like Appearance of Restricted Lower Limb Vasculitis on Fluorodeoxyglucose-positron Emission Tomography. Internal medicine (Tokyo, Japan) 2022. link 81 Kilduff S, Butler J, Sogawa H, Solomon S. Practice patterns and outcomes for pediatric ANCA vasculitis transplant recipients in a national cohort. 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Rheumatology international 2021. link 91 Gehlhausen JR, Wetter DA, Nelson C, Ramachandran S, McNiff JM, Ko CJ. A detailed analysis of the distribution, morphology, and histopathology of complex purpura in hospitalized patients: A case series of 68 patients. Journal of the American Academy of Dermatology 2021. link 92 Mustapha N, Barra L, Carette S, Cuthbertson D, Khalidi NA, Koening CL et al.. Efficacy of leflunomide in the treatment of vasculitis. Clinical and experimental rheumatology 2021. link 93 Pfeuffer-Jovic E, Heyckendorf J, Reischl U, Bohle RM, Bley T, Buck A et al.. Pulmonary vasculitis due to infection with Mycobacterium goodii: A case report. International journal of infectious diseases : IJID : official publication of the International Society for Infectious Diseases 2021. link 94 Mendel A, Ennis D, Carette S, Pagnoux C. Assessment of glucocorticoid tapering in large vessel and anti-neutrophil cytoplasmic antibody-associated vasculitides. Clinical and experimental rheumatology 2021. link 95 Singh JA. Infection versus cardiovascular disease as leading causes of hospitalisations and associated mortality in vasculitis in the U.S.: a national study. Clinical and experimental rheumatology 2021. link 96 Hiruma M, Sasano Y, Watanabe N, Yoshihara A, Ishii S, Yaguchi Y et al.. Propylthiouracil-induced otitis media with anti-neutrophil cytoplasmic antibody-associated vasculitis: a case report and review of the literature. Endocrine journal 2021. link 97 Takeyama Y, Ono N, Shirahama Y, Inoue Y, Tanaka A, Ueda N et al.. Rituximab maintenance therapy for patients with antineutrophil cytoplasmic antibody-associated vasculitis in Japan. Modern rheumatology 2021. link 98 Shibata A, Kondo T, Kurasawa T, Chino K, Okada Y, Amano K. A case of polyangiitis overlap syndrome of giant cell arteritis and granulomatosis with polyangiitis successfully treated with rituximab. 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