Overview
Arrhythmic mitral valve prolapse (AMVP) is a subset of mitral valve prolapse (MVP) associated with ventricular arrhythmias and sudden cardiac death 1. Identifying predictive factors for arrhythmic risk in MVP patients remains an area of ongoing research 1.Diagnosis
Bileaflet morphology is more common in AMVP compared to nonarrhythmic MVP 1.
Echocardiographic findings associated with AMVP include:
* Longer anterior and posterior mitral leaflets 1.
* Thicker anterior mitral leaflet 1.
* Mitral annular disjunction (MAD) 1.
Electrocardiographic findings associated with AMVP include T-wave inversion 1.
Cardiac magnetic resonance imaging findings associated with AMVP include late gadolinium enhancement (LGE) 1.
Increased mechanical dispersion is observed in AMVP 1.Management
No specific management strategies for AMVP are detailed in the provided abstracts.Key Recommendations
Bileaflet mitral valve prolapse is more represented in patients with arrhythmic mitral valve prolapse 1. (Evidence: Moderate)
T-wave inversion on electrocardiography is more represented in patients with arrhythmic mitral valve prolapse 1. (Evidence: Moderate)
Mitral annular disjunction is more represented in patients with arrhythmic mitral valve prolapse 1. (Evidence: Moderate)
Late gadolinium enhancement on cardiac magnetic resonance imaging is more represented in patients with arrhythmic mitral valve prolapse 1. (Evidence: Moderate)References
1 Pistelli L, Vetta G, Parlavecchio A, Crea P, Parisi F, Magnocavallo M et al.. Arrhythmic risk profile in mitral valve prolapse: A systematic review and metanalysis of 1715 patients. Journal of cardiovascular electrophysiology 2024. link